Expectations (prognosis)
If left untreated, hypoplastic left heart syndrome is fatal. Survival rates for the staged repair continue to rise as surgical technique and postoperative management improve. Survival after the first stage is more than 75%.
It is important to note that the size and function of the right ventricle are important determinants of outcome after surgery.
Complications
Complications include:
- Irregular, fast heart rhythms (arrhythmias)
- Chronic diarrhea
- Heart failure
- Fluid in the abdomen (ascites)
- Blockage of the artificial shunt
- Strokes and other neurological complications
- Sudden death
Calling your health care provider
If your infant has new changes in breathing patterns, eats less (decreased feeing), or has skin or mucous membranes that are turning blue (cyanotic), contact your health care provider immediately.
Prevention
There is no known prevention for hypoplastic left heart syndrome. As with many congenital diseases, the causes of hypoplastic left heart syndrome are uncertain and have not been linked to a mother's disease or behavior.